Tuberous sclerosis presenting with acute kidney failure, pyelonephritis, and polycystic kidney disease.

نویسندگان

  • Masoumeh Mohkam
  • Shirin Shohadaii
  • Farshid Kompani
  • Hamid Reza Aghadoost
  • Seyed Ali Hojati
  • Nasrin Esfandiar
چکیده

Tuberous sclerosis complex (TSC) is a multisystemic inherited autosomal dominant disease characterized by the development of hamartomas in the brain and kidneys. In about 2% of patients, polycystic kidney disease is present, which may result in different stages of renal insufficiency. Acute kidney failure has not been reported in infants with TSC. We report a female infant with TSC who was admitted to hospital with pyelonephritis, acute kidney injury, and polycystic kidney disease.

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Tuberous sclerosis presented with polycystic kidney disease and acute renal failure.

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عنوان ژورنال:
  • Iranian journal of kidney diseases

دوره 8 4  شماره 

صفحات  -

تاریخ انتشار 2014